Benign cephalic histiocytosis in Child
Synopsis

Involution of lesions occurs spontaneously over the ages of 2-8 years, often with residual postinflammatory hyperpigmentation that persists indefinitely. There have been no reported associated systemic diseases or reports of visceral involvement. Some experts consider BCH to be a childhood variant of generalized eruptive histiocytoma, and some reports suggest that BCH may have overlapping clinical and histologic features with juvenile xanthogranuloma (JXG). There have been reports of BCH transforming later into JXG, further establishing this theoretical overlap. BCH may be difficult to differentiate clinically from JXG, but key differentiating features are that BCH lesions tend to be flatter and are mainly on the head and neck.
Codes
D76.3 – Other histiocytosis syndromes
SNOMEDCT:
255192005 – Benign cephalic histiocytosis
Look For
Subscription Required
Diagnostic Pearls
Subscription Required
Differential Diagnosis & Pitfalls
Subscription Required
Best Tests
Subscription Required
Management Pearls
Subscription Required
Therapy
Subscription Required
References
Subscription Required