Malignant proliferating trichilemmal tumor
Synopsis

The diagnosis of MPTT is based mainly on histological features. A histological classification system has been proposed to differentiate the more common and benign proliferating trichilemmal tumor (PTT) from low-grade and high-grade MPTTs, which have potential for metastasis.
Recurrences are not uncommon. MPTT is at high risk for metastasis, with regional and distant metastatic disease in up to 25% of patients.
More than 40 cases of MPTT have been described in the literature, including 12 cases with metastatic disease and several mortalities.
Codes
C44.49 – Other specified malignant neoplasm of skin of scalp and neck
SNOMEDCT:
399878004 – Malignant neoplasm with pilar differentiation
446023005 – Proliferating trichilemmal tumor
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Last Updated:06/12/2019