Microscopic polyangiitis
Synopsis
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MPA most often occurs in patients between ages 50 and 60 years, but cases have been reported in children and older adults as well. There is a slight male predominance. MPA is most common in patients of Northern European descent.
Complications of MPA include diffuse alveolar hemorrhage, interstitial lung disease, pleural effusion, pulmonary edema, pleuritis, interstitial fibrosis, rapidly progressive focal segmental necrotizing glomerulonephritis, gastrointestinal bleeding, colonic ulcerations, intestinal ischemia, bowel perforation, mononeuritis multiplex, and polyneuropathy.
Codes
M31.7 – Microscopic polyangiitis
SNOMEDCT:
1144805008 – Microscopic polyangiitis
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Last Updated:07/27/2020